Type I pleuropulmonary blastoma presenting as congenital pulmonary airway malformation: A report of two cases
نویسندگان
چکیده
منابع مشابه
Pleuropulmonary Blastoma: Report of 2 Cases
Pleuropulmonary blastoma (PPB) is a rare, malignant intrathoracic tumor that occurs mostly in children before 5 years old. It consists about 15% of all primary pediatric pulmonary tumors and shows various mesenchymal components. Its presentations are nonspecific and common symptoms include fever, cough, chest pain, respiratory distress, and pulmonary infection. PPB should be considered in the ...
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Pleuropulmonary blastoma (PPB) is a rare aggressive malignant tumor of infancy and early childhood. The tumor arises in the lung and pleura and is regarded as a pulmonary dysontogenetic or embryonic neoplasm. Four types are defined in literature. Type I PPB is a rare, cystic lung neoplasm in infants characterized by subtle malignant changes and a good prognosis. Recurrences after type I PPB are...
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BACKGROUND Type I pleuropulmonary blastoma (PPB) and congenital cystic adenomatoid malformation of the lung (CCAM) are cystic lung diseases of childhood. Their clinical and radiological presentations are often similar, and pathologic discrimination remains difficult in many cases. As a consequence, type I PPB and CCAM are frequently confused, leading to delayed adequate management for type I PP...
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Pleuropulmonary blastoma is a rare and aggressive neoplasm typically presents in young children, younger than 5 years, as a pulmonary and/or pleural-based tumor. We reported a case of type-II pleuropulmonary blastoma (PPB) in an 8 month old infant who presented to Al-Khansa'a Maternity Hospital in Western Mosul with a history of repeated attacks of shortness of breath and signs of pulmonary inf...
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Congenital pulmonary airway malformation (CPAM) is a very rare pulmonary disease in children. It is often misdiagnosed as a persistent and localized pneumothorax without any further pathological diagnosis. Malignancy and frequent airway infections are major concerns in these patients. Surgical excision is recommended to make a definite diagnosis and exclude hidden malignancies, and is also the ...
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ژورنال
عنوان ژورنال: Indian Journal of Pathology and Microbiology
سال: 2019
ISSN: 0377-4929
DOI: 10.4103/ijpm.ijpm_713_18